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Lysosomal lipid and protein catabolism. Overview of the major lysosomal catabolic pathways and enzymes involved in the degradation of sphingolipids, glycerophospholipids, and cholesterol esters. For protein abbreviations see introduction to legend. Lipid abbreviations: Bis(monoacylglycero)phosphate (BMP), monosialotetrahexosylganglioside (GM1), GM2 ganglioside (GM2), monosialodihexosylganglioside (GM3), lactosylceramide (LacCer), glycosylceramide (GlcCer), galactosylceramide (GalCer), sulfatide (SM4), globo-triaosylceramide (GB3).
#Workflow#Pathway#Lysosome#Lipid Catabolism#Protein Catabolism#Sphingolipids#Glycerophospholipids#Cholesterol Esters#Lysosomal Acid Lipase/Cholesteryl Ester Hydrolase (LAL)#Lysosomal Phospholipase A and Acyltransferase (PLA, PLA2G15)#Putative Phospholipase B-Like 2 (PLB)#Beta-Galactosidase (GLB1)#Beta-Hexosaminidase Subunit Alpha (HEXA)#Beta-Hexosaminidase Subunit Beta (HEXB)#Ganglioside GM2 Activator (GM2A)#Sialidase-1 (NEU1)#Lysosomal Acid Glucosylceramidase (GBA1)#Acid Ceramidase (ASAH1)#Alpha-Galactosidase A (GLA)#Arylsulfatase A (ARSA)#Galactocerebrosidase (GALC)#Sphingomyelin Phosphodiesterase (SMPD1)#Bis(Monoacylglycero)Phosphate (BMP)#Monosialotetrahexosylganglioside (GM1)#GM2 Ganglioside (GM2)#Monosialodihexosylganglioside (GM3)#Lactosylceramide (LacCer)#Glycosylceramide (GlcCer)#Galactosylceramide (GalCer)#Sulfatide (SM4)#Globo-triaosylceramide (GB3)
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